Hughes-Stovin syndrome revealing the presence of Behçet’s Disease
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Melek Kechida , Sondes Yaacoubi , Ahmed Zrig , Walid Jomaa , Rim Klii , Sonia Hammami , Ines Khochtali |
Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia , kechida_mel_lek@hotmail.com |
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Abstract: (6703 Views) |
Background: Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen.
Case presentation: We report the first case of HSS with aortic aneurysm in a 55-year-old man who initially presented with deep venous thrombosis. The diagnosis of HSS revealing Behçet’s disease was made given the history of recurrent oral and genital ulcers. Treatment consisted of 3 daily pulses of methylprednisolone (1g) followed by oral prednisone (1mg/kg daily) and 6 monthly pulses of cyclophosphamide. Oral anticoagulation treatment was held 3 months and then was stopped with good outcome.
Conclusion: Systemic aneurysms in Hughes Stovin is a worth knowing complication which may reveal Behçet’s disease.
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Keywords: Behçet syndrome, Hughes-Stovin syndrome, Aortic aneurysm |
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Full-Text [PDF 209 kb]
(965 Downloads)
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Type of Study: case report |
Subject:
Internal Received: 2016/09/22 | Accepted: 2017/04/29 | Published: 2017/09/19
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