RT - Journal Article T1 - Hughes-Stovin syndrome revealing the presence of Behçet’s Disease JF - babol-caspjim YR - 2017 JO - babol-caspjim VO - 8 IS - 4 UR - http://caspjim.com/article-1-871-en.html SP - 332 EP - 334 K1 - Behçet syndrome K1 - Hughes-Stovin syndrome K1 - Aortic aneurysm AB - Background: Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen. Case presentation: We report the first case of HSS with aortic aneurysm in a 55-year-old man who initially presented with deep venous thrombosis. The diagnosis of HSS revealing Behçet’s disease was made given the history of recurrent oral and genital ulcers. Treatment consisted of 3 daily pulses of methylprednisolone (1g) followed by oral prednisone (1mg/kg daily) and 6 monthly pulses of cyclophosphamide. Oral anticoagulation treatment was held 3 months and then was stopped with good outcome. Conclusion: Systemic aneurysms in Hughes Stovin is a worth knowing complication which may reveal Behçet’s disease. LA eng UL http://caspjim.com/article-1-871-en.html M3 10.22088/cjim.8.4.332 ER -