en Surgery Surgery case report case report <span style="font-size:14px;"><span style="font-family:Times New Roman;"><span style="line-height:14pt"><b><i><span style="color:blue">Background:</span></i></b> Gallbladder agenesis is a biliary tract related congenital malformation with an incidence of 10&ndash;65 per 100,000 and associated with other congenital abnormalities. GA is usually asymptomatic, but sometimes patients become symptomatic. The most usual symptoms are jaundice, abdominal pain in the right upper quadrant, nausea and vomiting. We reported a case of GA and choledochogastric fistula in a patient with history of cholangitis.</span><br> <span style="line-height:14pt"><b><i><span style="color:blue">Case Presentation:</span></i></b> A 70-year-old man presented to Emergency Department of Modarres&nbsp;Hospital with jaundice, fever, right upper quadrant abdominal pain, nausea and vomiting. Clinical examination and lab test demonstrated cholangitis. He underwent ultrasonography, abdominopelvic CT scan and ERCP. ERCP revealed a CBD fistula. Due to recurrent symptoms, he underwent operation and hepaticojejunostomy was done.</span><br> <b><i><span style="color:blue">Conclusion:</span></i> </b>In our knowledge, the case of GA and choledochogastric fistula is rare. Furthermore, this type of abnormalities rarely presented with cholangitis, so probable anatomical malformation of the biliary tract should always be considered as a differential diagnosis in patients with <span lang="EN">biliary disease signs and symptoms</span></span></span> Gallbladder agenesis, choledochogastric fistula , cholangitis 751 754 http://caspjim.com/browse.php?a_code=A-10-2478-1&slc_lang=en&sid=1 Nasser Malekpour Alamdari nassermalekpour@gmail.com 100319475328460044983 100319475328460044983 No Department of General Surgery, Shahid Modarres Hospital, Shahid Beheshti University of medical sciences, Tehran, Iran Adel Zeinalpour adel.zeinalpour@gmail.com 100319475328460044984 100319475328460044984 Yes Department of General Surgery, Shahid Modarres Hospital, Shahid Beheshti University of medical sciences, Tehran, Iran Barmak Gholizadeh barmak.gholizadeh@gmail.com 100319475328460044985 100319475328460044985 No Department of General Surgery, Shahid Modarres Hospital, Shahid Beheshti University of medical sciences, Tehran, Iran Maryam Abbasi maryamabbasi1986@gmail.com 100319475328460044986 100319475328460044986 No Department of General Surgery, Shahid Modarres Hospital, Shahid Beheshti University of medical sciences, Tehran, Iran Faezeh Shams f_shams2020@yahoo.com 100319475328460044987 100319475328460044987 No Department of General Surgery, Shahid Modarres Hospital, Shahid Beheshti University of medical sciences, Tehran, Iran Hamed Ebrahimibagha H.ebrahimi@sbmu.ac.ir 100319475328460044988 100319475328460044988 No Department of General Surgery, Shahid Modarres Hospital, Shahid Beheshti University of medical sciences, Tehran, Iran