Kechida M, Yaacoubi S, Zrig A, Jomaa W, Klii R, Hammami S et al . Hughes-Stovin syndrome revealing the presence of Behçet’s Disease
. Caspian J Intern Med 2017; 8 (4) :332-334 URL: http://caspjim.com/article-1-871-fa.html
Hughes-Stovin syndrome revealing the presence of Behçet’s Disease
. . 1396; 8 (4) :332-334
Background: Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen. Case presentation:We report the first case of HSS with aortic aneurysm in a 55-year-old man who initially presented with deep venous thrombosis. The diagnosis of HSS revealing Behçet’s disease was made given the history of recurrent oral and genital ulcers. Treatment consisted of 3 daily pulses of methylprednisolone (1g) followed by oral prednisone (1mg/kg daily) and 6 monthly pulses of cyclophosphamide. Oral anticoagulation treatment was held 3 months and then was stopped with good outcome. Conclusion: Systemic aneurysms in Hughes Stovin is a worth knowing complication which may reveal Behçet’s disease.