Ghasemi Shektaie S H, Shafi H, Falahi A, Mahmoudlou F, Moudi E. A rare case of papillary cystadenoma of epididymis presented with painless scrotal mass. Caspian J Intern Med 2021; 12 (S2) :388-391
URL:
http://caspjim.com/article-1-2172-en.html
Cancer Research Center, Health Research Institute, Babol University of Medical Sciences, Babol, Iran , dr_hamidshafi@yahoo.com
Abstract: (2309 Views)
Background: Papillary cystadenoma of epididymis (PCE) is the second most common benign neoplasm of epididymis arises from the efferent ductules of the head of the epididymis. Totally, PCE is an asymptomatic condition with a mean age of diagnosis of thirties. It has two forms, the solitary form and Von Hippel-Lindau associated form. Unilateral PCE usually follows the solitary form but the bilateral is associated with Von Hippel-Lindau (VHL). Here we described a rare case of unilateral PCE presented with painless scrotal mass.
Case Presentation: A 37-year-old man presented with a history of unilateral painless scrotal mass for many years. However he had varicose veins, he has 8 y/o daughter. The examination was normal totally. The ultrasonography (US) of kidneys revealed multiple cysts in variable sizes in the cortex of the both kidneys. The US of scrotum demonstrated hypervascular multiple cysts in the head of the right epididymis. Its report emphasized on “the adhesion of these cysts to the upper pole of the right testis presenting a neoplastic mass”. The patient underwent radical right orchiectomy and the pathology studies revealed it was a unilateral PCE and suggested further investigations for VHL.
Conclusion: It seems that there is no useful guideline about this issue yet. In our patient, however he did not accept to pass the genetic testing studies and also his IHC studies were negative about VHLD but still had kind of a retinal hemangioma and a suspicious cerebellum mass which made him more probable to be a VHL case.
Type of Study:
case report |
Subject:
Internal Received: 2020/01/11 | Accepted: 2020/08/11 | Published: 2021/07/24